Congenital hepatic cyst: Eleven case reports

Chun-Xia Du1, Chang-Gui Lu1, Wei Li1

  • 1Department of Paediatric Surgery, Children's Hospital of Nanjing Medical University, Nanjing 210008, Jiangsu Province, China.

Insights

Congenital hepatic cysts in infants are rare but diagnosable early with imaging. Surgical unroofing is effective for symptomatic cases, leading to a good prognosis for infant liver cysts.

Area of Science:

  • Pediatric Surgery
  • Hepatology
  • Neonatal Imaging

Background:

  • Congenital hepatic cysts are uncommon pediatric conditions.
  • Early diagnosis is facilitated by advanced imaging techniques.
  • This study investigates clinical features, surgical management, and outcomes of infantile hepatic cysts.

Observation:

  • A case series of eleven infants with hepatic cysts was analyzed.
  • Ten infants had simple hepatic cysts (8 solitary, 2 multiple); one had a solitary intrahepatic biliary cyst with a choledochal cyst.
  • Most solitary hepatic cysts were detected prenatally and located in the right liver lobe.

Findings:

  • Symptomatic hepatic cysts necessitated surgical intervention.
  • Cyst resection or unroofing with fulguration was performed.
  • No cyst recurrence was observed post-intervention.

Implications:

  • Congenital hepatic cysts have a limited differential diagnosis requiring accurate assessment.
  • Surgical unroofing is the preferred treatment for symptomatic infantile cysts.
  • Infants with congenital hepatic cysts generally experience favorable outcomes.
Abstract

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