[Congenital cystoid dilatation of the intrahepatic bile ducts]

In the world literature there are descriptions of about 60 cases of the Caroli disease representing a congenital dilatation of intrahepatic bile ducts. Unlike true cysts of the liver the cystoid dilatation of the ducts in Caroli disease contains bile and features of chronic cholangitis prevail in the clinical picture of the disease. The diagnostics is difficult. Intraoperative cholangiography is the most informative method.