Intra-abdominal desmoplastic small blue round cell tumor: A case report

Desmoplastic small round blue cell tumors are a rare and aggressive type of malignant small round blue cell tumor with a limited number of cases published in the literature. They commonly affect males in their second decade of life who usually present with a metastasis picture, resulting in a poor prognosis. We present a case of an intra-abdominal desmoplastic small blue round cell tumor in a 23-year-old male who presented with abdominal pain and bloating. Computed tomography revealed a large intra-abdominal mass which was followed by laparotomy and surgical resection of the abdominal mass with histology confirming the diagnosis. Careful clinical, radiological, and histopathological correlations are crucial to reach an accurate diagnosis which would be followed by surgical cytoreduction with primary, partial or complete tumor removal.