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Mid-aortic Syndrome in a Pediatric Cohort
Laia Brunet-Garcia1, Fredy Hermógenes Prada Martínez2, Angela Lopez Sainz3
1Department of Paediatric Cardiology, Consorci Sanitari del Maresme, Hospital de Mataró, Barcelona, Spain.
Pediatric Cardiology
|October 28, 2022
Summary
Early blood pressure monitoring is vital for pediatric Mid-aortic syndrome (MAS) detection. Endovascular treatment shows promise as an alternative to surgery for MAS, but further research is needed.
Area of Science:
- Cardiology
- Pediatric Nephrology
- Vascular Surgery
Background:
- Mid-aortic syndrome (MAS) is a rare condition causing abdominal aorta narrowing, often affecting visceral and renal arteries.
- Untreated MAS can lead to hypertension and end-organ damage, particularly in pediatric patients.
Purpose of the Study:
- To review 8 new pediatric cases of Mid-aortic syndrome.
- To evaluate the effectiveness of different treatment modalities in pediatric MAS patients.
Main Methods:
- Retrospective observational study of pediatric MAS cases diagnosed between April 1992 and November 2021.
- Systematic evaluation including medical/family history, ECG, echocardiogram, and advanced imaging (angiography, CT/MR angiography).
Main Results:
- 8 pediatric patients with MAS were included, with a median diagnosis age of 2.6 years.
- Most patients presented with incidental hypertension; 7/8 underwent endovascular treatment, with varied blood pressure control outcomes.
- One patient underwent surgery, and one death occurred during the follow-up period.
Conclusions:
- Blood pressure monitoring is crucial for early pediatric MAS recognition.
- Endovascular treatment may be a viable alternative to surgery for pediatric MAS.
- Further large-scale, long-term studies are necessary to establish optimal treatment strategies.
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