Related Experiment Video

Updated: Aug 23, 2025

Cox-Maze IV Procedure Concomitant with Valvular Surgery In Situs Inversus Dextrocardia: A Single-Center Experience in China
08:42

Cox-Maze IV Procedure Concomitant with Valvular Surgery In Situs Inversus Dextrocardia: A Single-Center Experience in China

Published on: February 11, 2022

3.6K

Cor triatriatum sinister: Long-term surgical outcomes in children and a proposal for a new classification

Ali H Mashadi1, Shanti L Narasimhan2, Sameh M Said3,4

  • 1Department of Integrative Biology and Physiology, Undergraduate Studies, University of Minnesota, Minneapolis, Minnesota, USA.

Journal of Cardiac Surgery
|November 2, 2022
PubMed

Insights

Cor Triatriatum Sinister (CTS) is a rare congenital heart defect. This study of 16 children shows good outcomes with surgical intervention and emphasizes comprehensive classification for better diagnosis and family counseling.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Cor Triatriatum Sinister (CTS) is a rare congenital anomaly (0.4% incidence) caused by abnormal left atrial septation.
  • It can occur alone or with other heart defects, often requiring surgical correction.
  • Previous classifications exist, but a more comprehensive approach is needed.

Purpose of the Study:

  • To describe a case series of pediatric patients with Cor Triatriatum Sinister.
  • To propose a more comprehensive and inclusive classification for CTS.
  • To evaluate clinical presentations, surgical outcomes, and long-term follow-up.

Main Methods:

  • Single-center retrospective cohort study.
  • Reviewed medical records of 16 children diagnosed with CTS between 2000 and 2020.
  • Analyzed clinical presentations, hospital courses, and postoperative outcomes.

Main Results:

  • 16 patients (63% female), median age 4.3 months; 31% were neonates.
  • 38% had isolated CTS, 13% with single ventricle, 50% with other defects (e.g., ASD, CoA, PVAP).
  • 50% presented with obstructed CTS; 75% underwent surgery with a 19% mortality rate (surgical and non-surgical). Recurrence was 17%.

Conclusions:

  • Patients with isolated and complex CTS demonstrate favorable long-term outcomes.
  • A complete and accurate CTS classification aids diagnosis, surgical planning, and family counseling.
  • Improved classification may correlate with better patient outcomes.
Abstract

Keywords:
cardiovascular pathologycardiovascular researchcongenital heart disease

More Related Videos

Implantation of Total Artificial Heart in Congenital Heart Disease07:27

Implantation of Total Artificial Heart in Congenital Heart Disease

Published on: July 18, 2014

24.7K
A Rodent Model of The Ross Operation: Syngeneic Pulmonary Artery Graft Implantation in A Systemic Position11:20

A Rodent Model of The Ross Operation: Syngeneic Pulmonary Artery Graft Implantation in A Systemic Position

Published on: April 1, 2022

3.1K

Related Concept Videos

Mitral Stenosis III: Medical Management01:26

Mitral Stenosis III: Medical Management

Mitral stenosis, a condition marked by the narrowing of the mitral valve, necessitates an integrated approach for effective management. This approach includes preventative measures, medical therapy, and surgical interventions to reduce symptoms and prevent complications.PreventionPrevention of mitral stenosis primarily focuses on reducing the incidence of bacterial infections, particularly streptococcal infections, which can lead to rheumatic fever and subsequent valvular damage. Timely...
16
Mitral Stenosis I: Introduction01:22

Mitral Stenosis I: Introduction

Mitral Valve Stenosis (MVS) is a heart condition where the mitral valve narrows, impeding blood circulation from the left atrium to the left ventricle. The etiology and pathophysiology of this condition are multifaceted, leading to a cascade of cardiovascular complications.Causes of Mitral Valve StenosisRheumatic Heart Disease: It is the main cause of mitral valve stenosis, particularly in developing nations. This condition arises from rheumatic fever, an inflammatory illness resulting from...
26
Mitral Regurgitation III: Medical Management01:25

Mitral Regurgitation III: Medical Management

Mitral regurgitation (MR) is characterized by retrograde blood circulation from the left ventricle into the left atrium due to inadequate mitral valve closure. The severity of the condition, symptoms, and underlying cause determine treatment strategies.Monitoring and Pharmacological TreatmentPatients with mild to moderate MR typically do not need immediate intervention but regular monitoring to assess progression and guide treatment. Patients with mild MR should have an echocardiogram every 3-5...
25
Mitral Stenosis II: Clinical features and Diagnostic Tests01:23

Mitral Stenosis II: Clinical features and Diagnostic Tests

Mitral stenosis is a heart condition in which the mitral valve, which allows blood to flow from the left atrium to the left ventricle, becomes narrowed or stenotic. This narrowing hinders blood flow and leads to clinical symptoms requiring specific medical evaluations and management strategies. The following overview outlines the clinical symptoms, assessments, diagnostic findings, prevention methods, and treatments for mitral stenosis.Clinical ManifestationsDyspnea (shortness of breath): This...
29
Cardiomyopathy III: Hypertrophic Cardiomyopathy01:29

Cardiomyopathy III: Hypertrophic Cardiomyopathy

Hypertrophic cardiomyopathy, or HCM, is an autosomal dominant genetic disorder characterized by asymmetric left ventricular hypertrophy without ventricular dilation. It is more common in men and is typically diagnosed in young, athletic adults.EtiologyHCM is primarily genetic and is caused by mutations in genes encoding sarcomeric proteins. Researchers have identified over 1400 mutations across at least 11 different genes. Among these, the most frequently occurring mutations are found in the...
37
Aortic Regurgitation III: Medical Management01:25

Aortic Regurgitation III: Medical Management

Aortic regurgitation (AR) is when the aortic valve does not close or seal properly, leading to backward blood circulation from the aorta into the left ventricle during diastole. Common causes of AR include rheumatic heart disease, congenital valve defects, and aortic root dilation. Managing AR requires a multifaceted approach to alleviate symptoms, preserve left ventricular function, and address the underlying cause of the regurgitation. Patients with symptomatic AR or significant left...
32