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Infantile Bowel Obstruction in a Patient with Situs Inversus Totalis and Polysplenia: A Case Report
Abdullahi Yusuf Ali1, Ahmet Biyikli1, Abdishakur Mohamed Abdi1
1Department of Pediatric Surgery, Somalia Turkish Training and Research Hospital, Mogadishu, Somalia.
Insights
This case report details a rare infantile intestinal obstruction in a boy with situs inversus totalis and polysplenia. The condition involved malrotation, volvulus, and pulmonary hypertension, presenting complex management challenges.
Area of Science:
- Pediatric Surgery
- Gastroenterology
- Medical Genetics
Background:
- Infantile intestinal obstruction is a critical surgical emergency.
- Situs inversus totalis (complete reversal of visceral organs) and polysplenia (multiple spleens) are rare congenital anomalies.
- The co-occurrence of these conditions with intestinal obstruction presents significant diagnostic and therapeutic challenges.
Observation:
- A 2-month-old male infant presented with symptoms of intestinal obstruction.
- Imaging and surgical findings revealed intestinal malrotation and volvulus.
- The small intestine was encased in a thin, translucent omental sac, a highly unusual finding.
Findings:
- The patient exhibited situs inversus totalis, polysplenia, and pulmonary hypertension.
- Intestinal obstruction was confirmed to be caused by malrotation and volvulus.
- This represents the first reported case combining all these specific anomalies and complications.
Implications:
- This case highlights the complex interplay between congenital anomalies and gastrointestinal emergencies.
- Management strategies for such rare conditions require a multidisciplinary approach.
- Further research into the embryological origins and clinical management of these combined anomalies is warranted.
Abstract:
The infantile intestinal obstruction associated with situs inversus totalis and polysplenia is extremely rare, with only a few cases reported in the literature. Furthermore, the management of this association is complicated. We report a case of a 2-month-old boy with intestinal obstruction due to malrotation and volvulus with thin translucent omentum sac encasing the small intestine associated with situs inversus totalis, polysplenia, and pulmonary hypertension. To the best of our knowledge, this is the first case of situs inversus totalis with polysplenia, pulmonary hypertension, and intestinal obstruction due to malrotation and volvulus with thin translucent omentum sac encasing the small intestine.
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