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Extensive Idiopathic Calcinosis in a Child - A Diagnostic and Therapeutic Imbroglio
Dharmagat Bhattarai1, Aaqib Z Banday2, Pratap K Patra3
1Om Hospital and Research Centre, Kathmandu, Nepal.
Abstract:
Idiopathic calcinosis is a disorder characterized by diffuse calcium deposits at various sites of the body. Etiopathogenic associations are described with inherited disorders, connective tissue disorders, infections, tumors, trauma, and endocrine disturbances. No diagnostic tests or standard therapeutic guidelines are established for this entity. There is paucity of literature on idiopathic calcinosis. We describe a girl child with extensive calcinosis in the skin and around muscle bundles without any clinical and laboratory evidence for etiological associations. Aggressive treatment modalities resulted a notable improvement in lesions in index child. Growing evidence will help to establish the ground for understanding and developing standard therapy.
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