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Recognising ligamentous atresia in double aortic arch
Tyler Bendrick1, Dillon Polito1, Randy Richardson2
1Creighton University School of Medicine, Phoenix Regional Campus, Phoenix, AZ, USA.
Cardiology in the Young
|December 13, 2022
Summary
Ligamentous atresia of the left side of a double aortic arch is a rare vascular ring easily mistaken for other conditions. Computed tomographic angiography offers accurate diagnosis and surgical planning for this condition.
Area of Science:
- Cardiovascular Surgery
- Pediatric Cardiology
- Diagnostic Imaging
Background:
- Ligamentous atresia of the left side of a double aortic arch is a rare vascular ring.
- It can be misdiagnosed as a right-sided aortic arch on transthoracic echocardiography due to mirror-imaged branching.
Observation:
- Computed tomographic angiography (CTA) with 3D reconstruction is the preferred imaging modality for diagnosing double aortic arch.
- CTA allows for rapid acquisition, sedation-free imaging in all age groups, including neonates.
- It provides excellent visualization of the aortic arch and its branching pattern.
Findings:
- This case series presents six children diagnosed with this rare vascular ring using CTA.
- CTA facilitated accurate diagnosis and surgical planning for all patients.
- The study highlights the outcomes of these pediatric patients.
Implications:
- CTA is crucial for the accurate diagnosis and effective surgical planning of rare vascular rings like left-sided ligamentous atresia.
- This imaging technique improves patient outcomes by enabling timely and precise interventions.
- The findings underscore the importance of advanced imaging in pediatric cardiovascular care.
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