Related Experiment Videos
Proptosis, skull infarction, and retro-orbital and epidural hematomas in a child with sickle cell disease
A A Mallouh1, M Young, J Hamdan
1Department of Pediatrics, Dhahran Health Center, Saudi Arabia.
Clinical Pediatrics
|October 1, 1987
Insights
A Saudi child with sickle cell disease (SS) experienced rare complications including skull bone infarcts and hematomas. This case highlights unusual presentations of SS in pediatric patients.
Area of Science:
- Pediatric Hematology
- Neurology
- Ophthalmology
Background:
- Sickle cell disease (SS) is a genetic blood disorder common in Saudi Arabia.
- Complications of SS can affect multiple organ systems, including the brain and eyes.
Observation:
- A Saudi child with SS presented with bilateral periorbital swelling and right proptosis.
- The child also exhibited skull bone infarcts, a retro-orbital hematoma, and an epidural hematoma.
Findings:
- Skull bone infarcts are an uncommon finding in sickle cell disease patients.
- Retro-orbital and epidural hematomas are also rare complications associated with SS.
Implications:
- This case underscores the importance of considering rare neurological and ophthalmological complications in pediatric SS.
- Early recognition and management of these unusual SS manifestations are crucial for patient outcomes.
Abstract:
A Saudi child with homozygous sickle cell disease (SS) presented with bilateral periorbital swelling, right-sided proptosis, skull bone infarcts, and retro-orbital and epidural hematomas. The findings of skull bone infarcts, retro-orbital and epidural hematomas are rare in patients with sickle cell disease.