Oncocytic carcinoma of the plica semilunaris with orbital extension

A 76-year-old male had orbital extension and regional lymph node involvement from an oncocytic carcinoma thought to have arisen in the plica semilunaris of the left eye. Declining early orbital exenteration and radical neck dissection, the patient received radiation therapy. Although initial palliation was achieved, the lesion recurred 1 year later, with massive orbital involvement. Despite exenteration and chemotherapy, the patient expired within 6 months. Oncocytomas arise from transformed epithelial cells, generally in the medial canthal region. Oncocytic carcinoma of the ocular adnexa is extremely rare and no such lesion of the plica semilunaris has been reported.