Sudden cardiac death as a consequence of Cor triatriatum sinistrum in an adult

Area of Science:

• Cardiology
• Congenital Heart Disease
• Pathology

Background:

• Cor triatriatum sinistrum (CTS) is a rare congenital cardiac malformation characterized by a fenestrated membrane dividing the left atrium.
• This anomaly can impede blood flow, leading to symptoms of congestive heart failure, and may rarely manifest in adulthood.

Observation:

• This case report presents a rare instance of sudden cardiac death (SCD) in an adult patient.
• The SCD was attributed to the long-term sequelae of undiagnosed and untreated Cor triatriatum sinistrum.

Findings:

• This is the first reported case of sudden cardiac death directly linked to Cor triatriatum sinistrum.
• The findings highlight the potential for severe, fatal outcomes from this congenital heart defect, even in adulthood.

Implications:

• This case underscores the importance of considering rare congenital heart anomalies in the differential diagnosis of sudden cardiac death, particularly in younger adults.
• It emphasizes the need for timely diagnosis and management of Cor triatriatum sinistrum to prevent potentially fatal complications.
• Further research into the long-term prognosis and optimal management strategies for adult patients with Cor triatriatum sinistrum is warranted.