Coronary Stent Placement in an Interarterial Anomalous Right Coronary Artery: An Alternative Approach in a
Erik J Simon1, Mary Rodriguez Ziccardi1, Saagar Sanghvi1
1Department of Medicine, Division of Cardiology, College of Medicine, University of Illinois Chicago, IL, US.
Insights
Anomalous aortic origin of a coronary artery, a rare congenital heart defect, can cause sudden cardiac death. This case highlights percutaneous coronary intervention as a treatment option for patients with this anomaly and comorbidities preventing surgery.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Interventional Cardiology
Background:
- Anomalous aortic origin of a coronary artery (AAOCA) is a rare congenital anomaly.
- AAOCA can be an etiology for sudden cardiac death, but clinical significance varies.
- Surgical management with coronary unroofing is the standard for symptomatic individuals, but not all cases are suitable for surgery.
Purpose of the Study:
- To report a unique case of anomalous right coronary artery with interarterial course managed with percutaneous coronary intervention (PCI).
- To describe a novel mechanism of aborted sudden cardiac death in a patient with AAOCA and severe comorbidities.
Main Methods:
- Case report of a patient with anomalous right coronary artery and interarterial course.
- Management with percutaneous coronary intervention due to surgical contraindications (comorbidities).
- Analysis of the proposed mechanism involving aggravated pulmonary hypertension.
Main Results:
- Successful management of symptomatic anomalous right coronary artery with PCI.
- Identification of a unique mechanism of aborted sudden cardiac death involving pulmonary hypertension in a patient with comorbid pulmonary disease.
- Demonstration of PCI as a viable alternative to surgery in select AAOCA cases.
Conclusions:
- Percutaneous coronary intervention can be a safe and effective alternative to surgery for managing anomalous aortic origin of a coronary artery in patients with contraindications.
- Aggravated pulmonary hypertension in patients with comorbid pulmonary disease can precipitate sudden cardiac death in the setting of anomalous aortic origin of a coronary artery.
- This case underscores the importance of considering individual patient factors and comorbidities when determining the optimal management strategy for anomalous aortic origin of a coronary artery.
Abstract:
Anomalous aortic origin of a coronary artery is a rare congenital anomaly and potential aetiology for sudden cardiac death. However, the mere presence of this anomaly does not portend clinical significance, and there are many factors that contribute to limiting coronary blood flow in these patients. The standard of care for symptomatic individuals is surgical management with coronary unroofing although not all cases are amenable to surgery. We report the case of an anomalous right coronary artery with interarterial course managed by percutaneous coronary intervention due to surgical contraindication secondary to comorbidities. The proposed mechanism of action culminating in aborted sudden cardiac death is unique and involves aggravated pulmonary hypertension in an individual with severe comorbid pulmonary disease.
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