Bilateral Renal Lymphangiomatosis

Area of Science:

• Medical Science
• Pathology
• Radiology

Background:

• Lymphangiomatosis is a rare benign mesenchymal disorder characterized by lymphatic channel malformation and dilatation.
• Commonly affects the neck and axilla, but can occur in various internal organs.
• Renal lymphangiomatosis is an exceptionally rare variant involving the kidneys.

Observation:

• A case study of a 24-year-old female presenting with bilateral flank pain.
• Radiological examination revealed bilateral perinephric fluid collection with multiple septations.
• The patient was diagnosed with bilateral perirenal lymphangiomatosis.

Findings:

• The case highlights the occurrence of bilateral perirenal lymphangiomatosis, a rare renal manifestation.
• Imaging findings included bilateral perinephric fluid collections with internal septations.
• This presentation underscores the diverse anatomical locations of lymphangiomatosis.

Implications:

• This case expands the understanding of renal lymphangiomatosis presentations.
• Highlights the importance of considering rare conditions in differential diagnosis for flank pain and perinephric fluid.
• Contributes to the literature on benign mesenchymal disorders affecting the renal system.