[Imaging findings of supratentorial embryonal tumor with multilayered rosettes in children]

Y T Liu1, M J Zhu1, M Yang1

  • 1Department of Radiology, Children's Hospital of Nanjing Medical University, Nanjing 210008, China.

Zhonghua Yi Xue Za Zhi
|January 17, 2023
PubMed

Insights

Pediatric supratentorial embryonal tumors with multilayered rosettes (ETMR) typically present as large cystic and solid masses with calcifications. Recognizing these imaging features aids in the accurate diagnosis of ETMR in children.

Area of Science:

  • Pediatric Neuroradiology
  • Neuro-oncology
  • Oncopathology

Context:

  • Embryonal tumors with multilayered rosettes (ETMR) are rare, aggressive brain tumors predominantly affecting young children.
  • Accurate diagnosis of pediatric brain tumors is crucial for timely and appropriate treatment planning.

Purpose:

  • To analyze and summarize the characteristic imaging findings of pediatric supratentorial ETMR.
  • To correlate imaging features with clinical data for improved diagnostic accuracy.

Summary:

  • Seven cases of pediatric supratentorial ETMR (four males, three females; ages 2-6 years) were analyzed.
  • Typical imaging findings include large cystic and solid masses, calcification, significant mass effect, and mild peritumoral edema.
  • The solid components often exhibit heterogeneous, mild enhancement, aiding in differentiation.

Impact:

  • Highlights the value of specific imaging manifestations in the diagnosis of supratentorial ETMR.
  • Contributes to the understanding of rare pediatric brain tumors, potentially improving diagnostic workflows.

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