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Distinction between Mitochondrial Antibody-Positive and -Negative Primary Biliary Cholangitis
Venkata Vinod Kumar Matli1, David F Dies2, Sudha Pandit3
1Department of Internal Medicine, Christus Highland Medical Center, Shreveport, LA, USA.
Case Reports in Gastroenterology
|February 6, 2023
Summary
Antimitochondrial antibody-negative primary biliary cholangitis (AMA-neg PBC) is a variant of AMA-positive PBC. Recognizing and differentiating AMA-neg PBC is crucial for diagnosis and management, even with similar treatment outcomes.
Area of Science:
- Hepatology
- Autoimmune Disorders
- Immunology
Background:
- Primary biliary cholangitis (PBC) is an autoimmune liver disease.
- Antimitochondrial antibody-positive PBC (AMA-pos PBC) is the common form.
- Antimitochondrial antibody-negative PBC (AMA-neg PBC) is a less common variant.

