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New conjugated urinary metabolites in intermediate type maple syrup urine disease
1Department of Clinical Chemistry and Blood Coagulation, Karolinska Hospital, Stockholm, Sweden.
Clinica Chimica Acta; International Journal of Clinical Chemistry
|October 30, 1987
Abstract:
N-Lactylvaline, N-lactylleucine, N-lactylisoleucine and the N-2-hydroxyisovaleryl conjugates of glycine, valine, leucine and isoleucine have been identified in urine from a patient with the intermediate type of maple syrup urine disease.