Related Experiment Video
Updated: Aug 10, 2025

Wireless Telemetry Device Implantation in a Fontan Ovine Model for Continuous and Long-Term Hemodynamic Monitoring
Published on: May 2, 2025
Considerations for Advanced Heart Failure Consultation in Individuals With Fontan Circulation: Recommendations From
Adam M Lubert1, Ari Cedars2, Christopher S Almond3
1Cincinnati Children's Hospital Heart Institute, Department of Pediatrics, University of Cincinnati College of Medicine, OH (A.M.L., A.L., D.L.S.M., L.S.).
Insights
Individuals with Fontan circulation face risks of death from heart and non-heart issues. New guidelines from the ACTION Fontan Committee aim to improve timely referrals for advanced heart failure care, addressing a critical gap.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Individuals with Fontan circulation have increased risks of late mortality from cardiac and noncardiac causes.
- Current referral indications for advanced heart failure care in this population are inconsistent, leading to delayed or missed consultations.
- This can result in preventable deaths from Fontan circulation-related complications.
Purpose of the Study:
- To establish clear, evidence-based guidelines for timely referral to advanced heart failure care for individuals with Fontan circulation.
- To provide primary cardiologists with recommended thresholds for referral based on clinical Fontan circulatory dysfunction.
- To reduce late mortality by ensuring appropriate and prompt access to advanced therapies.
Main Methods:
- Development of consensus-based recommendations by the Advanced Cardiac Therapies Improving Outcomes Network (ACTION) Fontan Committee.
- Categorization of clinical Fontan circulatory dysfunction into four key areas: cardiac/systemic ventricular dysfunction, Fontan pathway dysfunction, lymphatic dysfunction, and extracardiac dysfunction.
- Establishment of specific thresholds within these categories to guide advanced heart failure referral.
Main Results:
- The ACTION Fontan Committee has proposed specific recommendations for advanced heart failure referral.
- These recommendations are structured around four categories of Fontan circulatory dysfunction.
- The guidelines aim to standardize and optimize the timing of consultations for advanced heart failure therapies.
Conclusions:
- There is a critical need for standardized guidelines for advanced heart failure referral in individuals with Fontan circulation.
- The ACTION Fontan Committee's recommendations provide a framework to guide cardiologists in identifying patients who require timely consultation.
- Implementing these guidelines has the potential to improve outcomes and reduce mortality in this high-risk population.
Abstract:
Individuals with Fontan circulation are at risk of late mortality from both cardiac and noncardiac causes. Despite the known risk of mortality, referral indications for advanced heart failure care vary between centers, and many individuals die from Fontan circulation-related complications either after late consideration for advanced heart failure therapies or having never seen a heart failure specialist. There is a critical need for guidelines to direct appropriately timed referral for advanced heart failure consultation. The Advanced Cardiac Therapies Improving Outcomes Network (ACTION) Fontan Committee has developed recommended thresholds for advanced heart failure referral to guide primary cardiologists. These recommendations are divided into 4 categories of clinical Fontan circulatory dysfunction including (1) cardiac/systemic ventricular dysfunction, (2) Fontan pathway dysfunction, (3) lymphatic dysfunction, and (4) extracardiac dysfunction.
Related Concept Videos
Heart Failure VI: Adjunct Therapies
Heart Failure V: Medical Management
Heart Failure VII: Nursing Interventions
Heart Failure IV: Classification and Diagnostic Evaluation
Mitral Regurgitation IV: Nursing Management
Aortic Regurgitation IV: Nursing Management

