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Splenomegaly in Kawasaki Disease: A Pitfall in Diagnosis
Francesca Miselli1, Maria Vincenza Mastrolia2, Gabriele Simonini3
1Department of Health Sciences, University of Florence, Florence, Italy.
Abstract:
Among the 365 children diagnosed as having Kawasaki disease (KD), only 5 children (1.4%) presented with splenomegaly: 2 complicated by macrophage activation syndrome and 3 ultimately received a diagnosis of alternative systemic illness. Splenomegaly is atypical in KD and a potential marker of an underling complication, namely macrophage activation syndrome, or diagnosis other than KD.
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