Recurrent pericardial effusion in a boy: A clue to underlying pericardial and pulmonary lymphangiectasia

Deepanjan Bhattacharya1, Arun Gopalakrishnan1, Deepa Sasikumar1

  • 1Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, Kerala, India.

Insights

Pulmonary lymphangiectasia, a rare lymphatic vessel malformation, can cause recurrent pericardial effusion. This case highlights the link between this congenital condition and fluid buildup around the heart in children.

Area of Science:

  • Pediatric Cardiology
  • Thoracic Surgery
  • Medical Genetics

Background:

  • Pulmonary lymphangiectasia is a rare congenital lymphatic malformation.
  • Congenital lymphatic anomalies can affect multiple organ systems.
  • Pericardial effusion is excess fluid accumulation around the heart.

Observation:

  • A 5-year-old boy presented with recurrent pericardial effusion.
  • Diagnostic workup was performed to determine the cause of the effusion.

Findings:

  • The pericardial effusion was diagnosed as stemming from pericardial lymphangiectasia.
  • Pulmonary lymphangiectasia was also identified as a co-existing condition.

Implications:

  • This case underscores the importance of considering congenital lymphatic anomalies in pediatric recurrent pericardial effusion.
  • Early diagnosis and management of pulmonary lymphangiectasia may prevent cardiac complications.
  • Further research into the pathogenesis and treatment of lymphatic malformations is warranted.

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