Arterial switch for double-outlet left ventricle - Diagnostic and surgical considerations

Area of Science:

• Cardiology
• Pediatric Cardiac Surgery

Background:

• Double-outlet left ventricle (DOLV) is a rare congenital cardiac anomaly.
• It is characterized by both great arteries originating from the left ventricle.
• DOLV presents as a spectrum with variations in VSD position and outflow tract obstruction.

Observation:

• A 31-day-old neonate weighing 2.1 kg presented with DOLV and a subaortic ventricular septal defect (VSD).
• The neonate had no tricuspid atresia or hypoplastic right ventricle.

Findings:

• The neonate underwent a successful arterial switch operation with VSD closure.
• This surgical approach is preferred for two-ventricle repair in select DOLV cases.

Implications:

• This successful surgical outcome demonstrates the feasibility of a two-ventricle repair for complex DOLV.
• The arterial switch with VSD closure offers a viable treatment strategy for neonates with DOLV and subaortic VSD.
• This case contributes to the understanding and management of rare congenital heart defects.