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Published on: August 24, 2018
Bilateral, Solitary, Extramacular Vitelliform Retinal Lesions in a Patient With Best Disease
Jacob Duker1, Nimesh A Patel1, Nicolas A Yannuzzi1
1Department of Ophthalmology, Miller School of Medicine, Bascom Palmer Eye Institute, University of Miami, Miami, FL, USA.
Purpose:
This work describes the first published case of Best vitelliform macular dystrophy (BVMD) with bilateral, solitary, extramacular retinal lesions.
Methods:
A case report is presented.
Results:
An 8-year-old girl with a family history of BVMD was referred for suspicious peripheral retinal lesions. Multimodal imaging disclosed bilateral, solitary, extramacular lesions consistent with the vitelliform lesions found in BVMD. There were no abnormalities in the macula.
Conclusions:
This is the first documented case of solitary, bilateral, extramacular vitelliform lesions in BVMD.
