A Report of a Rare Case of Multiple Fibro adipose Venous Anomaly

Although not described more than a decade ago, fibro adipose vascular anomaly has grown of increasing importance as conventional management of arterio venous malformation with interventional radiology measures carry little success and cause significant morbidity in pediatric age groups like the case report we present here. Surgical resection, even though requiring significant loss of muscle bulk, is the mainstay of the treatment.

An 11-year-old patient presented with equinus deformity and intensely tender calf and foot swellings in the right leg. Magnetic resonance imaging showed presence of two distinct lesions, one involving the gastrocnemius and soleus, and the other in the Achilles tendon for which en bloc resection of the tumor was performed. Histopathology of the specimens confirmed the diagnosis of fibro adipose venous anomaly.

As per our knowledge, this is the first case of multiple fibro adipose venous anomaly confirmed by clinical features, radiology, and histopathology.