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Updated: Aug 2, 2025

Three-Dimensional Printing of a Complex Aortic Anomaly
Published on: November 1, 2018
Cardiac computed tomography assessment of congenital aortic diseases: a case series
Nilda Espinola-Zavaleta1,2, Javier Ivan Armenta-Moreno1, Jorge Alberto Silva-Estrada3
1Department of Nuclear Cardiology, National Institute of Cardiology Ignacio Chavez, Juan Badiano Nº 1, Colonia Seccion XVI, Tlalpan, 14080 Mexico City, Mexico.
Insights
Congenital aortic diseases present diverse symptoms and require advanced imaging. Cardiac computed tomography angiography is crucial for surgical planning in these complex aortic arch and vascular ring conditions.
Area of Science:
- Cardiology
- Medical Imaging
- Pediatric Surgery
Background:
- Congenital aortic diseases (CAoD) represent a spectrum of conditions affecting the aorta, varying from mild to critical.
- Accurate diagnosis and management are essential due to the potential for severe, life-threatening outcomes.
Observation:
- Seven case reports detail congenital aortic diseases, including aortic arch obstructions (coarctation, hypoplasia, interruption) and vascular rings.
- Clinical manifestations across these cases exhibit significant heterogeneity, underscoring the varied presentations of CAoD.
Findings:
- Multi-imaging modalities are vital for comprehensive CAoD assessment.
- Cardiac computed tomography angiography (CCTA) provides rapid, high-resolution 3D imaging, optimizing surgical planning.
Implications:
- Early and precise diagnosis through advanced imaging is critical for timely intervention.
- Understanding symptom heterogeneity aids in prompt recognition and management of congenital aortic diseases.
- CCTA facilitates improved surgical strategies for complex aortic pathologies.
Background:
Congenital aortic diseases (CAoD) encompass a wide variety of disorders that range from asymptomatic findings to life-threatening conditions. Multiple imaging techniques are available for the assessment of CAoD.
Case Summary:
We present seven case reports of congenital aortic diseases, including obstructions in the aortic arch (coarctation, hypoplasia, and interruption) and vascular rings, in which the clinical manifestations throughout the cases are discussed, highlighting the heterogeneity of the symptoms.
Discussion:
Multi-imaging techniques are indispensable for the assessment of CAoD, where cardiac computed tomography angiography is the main modality for rapid acquisition of three-dimensional volume-rendered images for optimal surgical planning.
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