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[A case of multiple duodenal gastrointestinal stromal tumors associated with neurofibromatosis type 1]
Yoshie Usami1, Tsunehiko Maruyama2, Naoaki Konno1
1Department of Gastroenterology, Mitosaiseikai General Hospital.
Abstract:
Gastrointestinal stromal tumors (GISTs) associated with von Recklinghausen's disease (neurofibromatosis type 1 [NF1]) have different pathogenesis and characteristics from common GISTs. Furthermore, no treatment strategy for this type of GIST has been established. This study presents the case of a 76-year-old man previously diagnosed with NF1 who was later diagnosed with GISTs. A resection of the horizontal leg of the duodenum was performed, and no recurrence was observed 18 months after the surgery.