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Heterotopic Auxiliary Whole Liver Rat Transplant Model Utilizing a Hepaticoureterostomy for Allograft Rejection Studies
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Hereditary Angioedema Post-liver Transplant.
Yusriya Al Rawahi1,2, Melanie Wong3, Michael Stormon1
1From the Department of Gastroenterology, The Children's Hospital at Westmead, Corner Hawkesbury Road and Hainsworth Street, Westmead, NSW.
JPGN Reports
|May 19, 2023
Summary
Liver transplantation can rarely transmit metabolic disorders. This case highlights acquired hereditary angioedema developing post-transplant, improving with C1 esterase inhibitor therapy.
Area of Science:
- Hepatology and Transplant Medicine
- Clinical Immunology and Genetics
Background:
- Liver transplantation is a primary treatment for liver diseases and inborn errors of metabolism (IEMs).
- While correcting metabolic defects, liver grafts can rarely transmit IEMs to recipients.
- Hereditary angioedema (HAE) is a rare genetic disorder affecting complement system regulation.
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