Percutaneous sequential closure of an Abernethy malformation: A case report
Asad Malik1, Muhammed Ebrahim Patel1, Daniel Ganger2
1Division of Interventional Radiology, Department of Radiology, Northwestern University, 676 N. St. Clair, Suite 800, Chicago, IL, USA.
Radiology Case Reports
|June 30, 2023
Summary
Abernethy malformation, a rare congenital extrahepatic portosystemic shunt (CEPS), can cause neurological symptoms. This case highlights successful endovascular closure using metal stents for effective management.
Area of Science:
- Vascular Surgery
- Interventional Radiology
- Pediatric Surgery
Background:
- Abernethy malformation, a congenital extrahepatic portosystemic shunt (CEPS), involves abnormal connections between portal and systemic veins, bypassing liver circulation.
- CEPS is rare, often diagnosed incidentally, and can lead to severe complications if untreated, including neurological deficits.
Observation:
- A case of Abernethy malformation was diagnosed via abdominal computed tomography.
- The patient presented with neurological symptoms, indicating a potential systemic impact of the shunt.
Findings:
- Successful management was achieved through interventional radiology.
- Endovascular closure was performed using sequential occlusion of two metal stents, effectively closing the aberrant connection.
Implications:
- This case demonstrates the efficacy of endovascular stent occlusion for managing Abernethy malformation.
- Interventional radiology offers a minimally invasive approach for treating CEPS, preventing potential complications like thrombosis.
