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Novel and Innovative Hybrid Technique for Type A Aortic Dissection
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391
Aortic Dissection in a Young Patient With Unsuspected Aortopathy
Yalile Perez1, M Yasir Qureshi1, Dusica Babovic-Vuksanovic2
1Department of Pediatric and Adolescent Medicine, Division of Pediatric Cardiology.
Pediatrics
|July 14, 2023
Summary
Aortic dissection is a rare but life-threatening condition in adolescents. Early diagnosis through comprehensive history and family screening is crucial for survival, especially in connective tissue disorders like Loeys-Dietz syndrome.
Area of Science:
- Cardiovascular Medicine
- Pediatric Cardiology
- Genetics
Background:
- Aortic dissection is a critical cardiovascular emergency with high mortality.
- It is exceptionally rare in pediatric populations.
- Severe aortic root dilation can predispose individuals to aortic dissection.
Purpose of the Study:
- To report a rare case of a surviving adolescent with aortic dissection.
- To highlight the importance of early diagnosis in pediatric aortic emergencies.
- To emphasize the link between connective tissue diseases and aortic dissection.
Main Methods:
- Case report of an adolescent male with aortic dissection.
- Review of clinical presentation, diagnostic workup, and management.
- Emphasis on comprehensive history and physical examination, including family history.
Main Results:
- The adolescent patient survived a severe aortic dissection.
- The dissection was associated with significant aortic root dilation.
- Connective tissue diseases, such as Loeys-Dietz syndrome, were considered.
Conclusions:
- Prompt recognition and emergent treatment are vital for survival in aortic dissection.
- Comprehensive patient evaluation, including family history, aids in diagnosing underlying connective tissue disorders.
- Loeys-Dietz syndrome is a critical consideration in adolescents presenting with aortic root dilation and dissection.
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