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Updated: Jul 21, 2025

Echocardiographic Evaluation of Atrial Communications before Transcatheter Closure
Published on: February 8, 2022
Idiopathic enlargement of the right atrium masking left atrial aneurysm in a neonate
N Forderer1, H Akintürk1, C Jux1
1Department of Pediatric Cardiology and Pediatric Cardiac Surgery, Pediatric Heart Center, University of Giessen, Giessen, HE, Germany.
Insights
Idiopathic right atrial enlargement is rare, with no clear management guidelines. This case study details a neonate
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Malformations
Background:
- Idiopathic enlargement of the right atrium is an extremely rare cardiac malformation.
- Established management guidelines for this condition are lacking, particularly regarding medical versus surgical approaches and optimal timing for intervention.
- This rarity poses significant challenges for clinical decision-making.
Purpose of the Study:
- To report a case of idiopathic right atrial enlargement in a neonate.
- To discuss the management challenges and outcomes associated with this rare condition.
- To highlight the complexities of surgical intervention and potential postoperative complications.
Main Methods:
- Conservative management was initiated in a neonate diagnosed with idiopathic right atrial enlargement.
- Surgical resection of the right atrial aneurysm was performed at 5 months of age.
- Postoperative monitoring and evaluation were conducted to assess outcomes and detect complications.
Main Results:
- The neonate initially received conservative treatment for 5 months.
- Surgical resection of the right atrial aneurysm was performed.
- Unexpected complications arose post-surgery, including the demasking of a second aneurysm in the left atrium.
- Progressive dilatation of both atrial chambers was observed, necessitating ongoing monitoring.
Conclusions:
- The management of idiopathic right atrial enlargement in neonates is complex and lacks established protocols.
- Surgical intervention, while sometimes necessary, carries risks of unexpected complications and de novo malformations.
- Long-term follow-up and continuous evaluation are crucial for patients with atrial aneurysms, especially after surgical resection.
Abstract:
An idiopathic enlargement of the right atrium is an extremely rare cardiac malformation. There are no established guidelines for the management of this disease, especially concerning medical versus surgical therapeutic approach and the timing for an operation. We report in this case about a neonate that first was treated conservatively until the age of 5 month and finally got an operative resection of the aneurysm. After surgery, unexpected complications occurred. A second aneurysm in the left atrium was demasked. Furthermore, a progressive dilatation of both atrial chambers after resection required regular follow-up and ongoing evaluation of treatment.
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