Congenital pulmonary airway malformation complicated by aspergilloma: A rare adulthood presentation - Case report

Rihab Molah1, Nasser Altowairqi2, Bader Alotaibi2

  • 1College of Medicine, King Saud University, Riyadh, 13315, Saudi Arabia.

PubMed

Insights

Congenital Pulmonary Airway Malformation (CPAM) in adults is rare, often presenting with fever and lung abscesses. This case highlights CPAM complicated by aspergilloma, successfully treated with surgery.

Area of Science:

  • Pulmonology
  • Thoracic Surgery
  • Infectious Diseases

Background:

  • Congenital Pulmonary Airway Malformation (CPAM) is a rare congenital lung malformation.
  • Adult presentation of CPAM is uncommon, often mimicking infectious processes like lung abscesses.

Observation:

  • A 39-year-old female presented with hemoptysis, a symptom not typical for uncomplicated CPAM.
  • Imaging revealed a CPAM in the right upper lobe complicated by an aspergilloma, a fungal ball within a pre-existing cavity.

Findings:

  • The patient had a right upper lobectomy to address the symptomatic CPAM and aspergilloma.
  • Post-operative follow-up confirmed the patient is symptom-free, indicating successful surgical management.

Implications:

  • This case underscores the importance of considering CPAM in adult patients presenting with respiratory symptoms, even if atypical.
  • Surgical resection remains an effective treatment for symptomatic CPAM and associated complications like aspergilloma.
  • Early diagnosis and intervention can lead to favorable outcomes in adult CPAM cases.

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