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Cochlear Implantation in Children with Additional Disabilities: A Systematic Review
Valeria Caragli1, Daniele Monzani2, Elisabetta Genovese3
1Otorhinolaryngology-Head and Neck Surgery, Audiology Program, Department of Diagnostic Clinical and Public Health, University of Modena and Reggio Emilia, 41125 Modena, Italy.
Children (Basel, Switzerland)
|October 28, 2023
Summary
Cochlear implants (CIs) benefit deaf or hard of hearing (DHH) children with disabilities, improving environmental awareness and adaptive skills. Language development may lag compared to DHH children without additional disabilities.
Area of Science:
- Pediatric Otolaryngology
- Developmental Pediatrics
- Neuroscience
Background:
- Cochlear implantation (CI) is a common intervention for children who are deaf or hard of hearing (DHH).
- The impact of CI in DHH children with co-occurring disabilities is less understood.
- Understanding benefits and challenges is crucial for optimizing outcomes in this population.
Purpose of the Study:
- To systematically review the last decade of literature on CI benefits for DHH children with additional disabilities.
- To identify specific benefits and challenges associated with CI in this complex pediatric population.
- To highlight areas for future research and personalized intervention strategies.
Main Methods:
- Systematic literature search conducted in PubMed, Embase, Scopus, PsycINFO, and Web of Science (January 2012 - July 2023).
- Two-stage search strategy to identify relevant studies.
- Inclusion of 61 articles focusing on CI in DHH children with diverse disabilities (e.g., ASD, CP, visual impairment).
Main Results:
- Many DHH children with additional disabilities demonstrated improved environmental sound awareness post-CI.
- Enhanced non-verbal communication and adaptive skills were observed, facilitating social interaction and environmental connection.
- Expressive language development showed improvement but lagged compared to DHH children without additional disabilities.
Conclusions:
- Cochlear implantation offers significant benefits in environmental awareness and adaptive skills for DHH children with co-occurring disabilities.
- Language acquisition requires tailored approaches, acknowledging slower progress in some cases.
- Further research is needed to understand individual disability impacts and develop validated tools for assessing quality of life and developmental trajectories.

