Kasabach-Merritt syndrome with disseminated intravascular coagulopathy treated by exchange transfusion and surgical excision
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Kasabach-Merritt syndrome, a rare condition causing low platelets, was treated in an infant with a back hemangioma. Surgical removal of the hemangioma led to complete recovery, highlighting its effectiveness over other therapies.
Area of Science:
- Pediatric Surgery
- Hematology
- Oncology
Background:
- Kasabach-Merritt syndrome (KMS) is a rare condition characterized by a vascular tumor and severe coagulopathy.
- Consumption coagulopathy, specifically disseminated intravascular coagulopathy (DIC), is a life-threatening complication of KMS.
Abstract:
Kasabach-Merritt syndrome with consumption coagulopathy occurred in a 5-week-old female infant with a hemangioma on her back. Disseminated intravascular coagulopathy was improved by an exchange transfusion. Administration of steroid and radiation therapy was attempted as a treatment for the hemangioma and thrombocytopenia; however, it was unsuccessful. Complete recovery was obtained by surgical excision. Enhanced computerized tomography was advantageous to determine the size of the hemangioma prior to operation.