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Cervical Aggressive Fibromatosis Causing Airway Obstruction
Azer Chebil1,2, Mehdi Hasnaoui1,2, Mohamed Masmoudi1,2
1Department of Otorhinolaryngology-Head and Neck Surgery, Taher Sfar University Hospital, Mahdia, Tunisia.
Ear, Nose, & Throat Journal
|November 10, 2023
Summary
Aggressive fibromatosis in the head and neck is rare but serious. This case highlights successful treatment with corticosteroids and antihormonal therapy for cervical fibromatosis causing obstructive dyspnea.
Area of Science:
- Oncology
- Pathology
Background:
- Fibromatosis, also known as desmoid tumors, are rare benign fibroblastic lesions.
- These tumors rarely occur in the head and neck but can be aggressive, leading to significant morbidity and mortality.
Purpose of the Study:
- To report a rare case of aggressive cervical fibromatosis presenting with acute obstructive dyspnea.
- To discuss the management and outcome of this rare condition in the head and neck region.
Main Methods:
- Case report of a 26-year-old female with cervical swelling and obstructive dyspnea.
- Diagnostic workup including pathological analysis of tissue samples.
- Treatment with corticosteroids and antihormonal therapy.
Main Results:
- Pathological analysis confirmed an aggressive fibromatosis.
- Emergency tracheotomy was required due to obstructive dyspnea.
- The patient responded well to medical treatment, with significant shrinkage of the fibrous mass and successful decannulation. No recurrence was observed during follow-up.
Conclusions:
- Aggressive fibromatosis in the cervical region is a rare entity with potentially severe consequences.
- Corticosteroids and antihormonal therapy can be effective in managing cervical fibromatosis.
- Further research is needed due to the lack of established therapeutic guidelines for this rare condition.
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