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Neuro-rehabilitation Approach for Sudden Sensorineural Hearing Loss
Published on: January 25, 2016
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Risk factors and outcomes in patients with cochlear nerve deficiency
Meagan Nowariak1, Natalie Strack2, Lindsey Greenlund1
1University of Minnesota Medical School, Minneapolis, MN, USA.
International Journal of Pediatric Otorhinolaryngology
|December 6, 2023
Summary
Cochlear nerve deficiency (CND) is linked to maternal diabetes and NICU stays. Hearing outcomes vary with amplification, including cochlear implantation (CI), requiring further research for CND patients.
Area of Science:
- Pediatric Otolaryngology
- Neuroscience
- Genetics
Background:
- Cochlear nerve deficiency (CND) is a radiologically defined cause of sensorineural hearing loss.
- Limited data exists on audiological outcomes and cochlear implantation (CI) success in CND patients.
Purpose of the Study:
- To investigate audiological outcomes and hearing device efficacy in patients with CND.
- To identify potential risk factors associated with CND.
Main Methods:
- Retrospective chart review of sensorineural hearing loss patients (2000-2020) at a children's hospital.
- Inclusion of patients with CND identified via imaging, categorized as hypoplastic, aplastic, or indeterminate.
- Analysis of hearing aid use (conventional, bone-anchored) and CI outcomes.
Main Results:
- 53 patients (70 ears) with CND were identified; 23.4% required NICU admission, and 15% had mothers with diabetes.
- Hearing devices used included conventional hearing aids (70%), bone-anchored hearing aids (17.1%), and CI (14.3%).
- Among 10 CI cases, 80% showed improved pure tone averages and 60% improved speech awareness thresholds.
Conclusions:
- Potential associations found between CND and maternal diabetes/NICU admission.
- Variable hearing outcomes observed with different amplification strategies in CND.
- Further research is necessary to clarify the role of CI, bone-anchored, and conventional hearing aids for CND.
