Chondromyxoid fibroma of the petrous-sphenoid junction

A case of primary chondromyxoid fibroma of the petrous and sphenoid bones extending into the posterior clinoid process, sella, and cavernous sinus in a 26-year-old man is reported. The presence of this tumor was heralded solely by the progressive paresis of the abducens nerve. The occurrence of this tumor is exceedingly rare, and to our knowledge, this is the first report of a primary chondromyxoid fibroma in the parasellar region. The natural history of this tumor, its pathologic diagnosis, and its treatment will be discussed with reference to this unusual case.