[Genital tract anomalies in anorectal malformations]

Of 131 patients with imperforate anus, 16 girls (25%), 10 boys (15%) have an abnormality of the genital tract and real frequency seems under evaluate. In girls, vaginal septum, bicornuate and didelphys uterus are mostly diagnosed, associated with severe unilateral upper urinary tract malformations. Absent vagina and uterus (Rokitansky syndrome) must be seen at birth, to preserve perineal fistula used to fashion a vagina at the time of the abdomino-perineal pull through. In our 3 cases upper urinary tract was normal. In boys, uretero-vas deferens anastomosis must be documented by vesiculo-deferentography when orchi-epididymitis or unilateral renal agenesis is demonstrated.