[Ocular hypotonia and retinal injuries in Steinert disease. Angiographic aspects]

The authors study ocular complications, mainly retinal, in three patients with myotonic dystrophy. The association of cataract, ocular hypotony, reticular or butterfly-shaped dystrophy of the macular pigmentary epithelium was observed in all cases. A bibliographical study regarding retinal lesions: clinical aspects (macular lesions and peripheral retinopathy), retinal functions (visual acuity, color sense, dark adaptation, electrophysiological examinations), histopathological aspects with proliferation of peripheral pigmentary epithelium, retinal and choroidal fibrohyalinosis. The authors report vitreous and retinal modifications (disc, macula, retinal vessels, peripheral retinopathy), evolutive aspects, electrophysiological anomalies in order to understand at best Steinert's ocular lesions.