[Sequential surgery in familial hyperlipemia. Comments on 2 pediatric cases]

The present report analyzes two cases of homozygotic familiar hypercholesterolemia. An actualization on the etiopathogenesis, the poor short term prognosis and the bad results obtained with the conservative therapy are discussed. The different surgical approaches excluding liver transplantation are reviewed. Both cases underwent staged portocaval shunts and ileal exclusions afterwards. Short and intermediate results are exposed.