Is it double chambered left ventricle? Unveiling the mirage using cardiac magnetic resonance imaging

Digvijay D Nalawade1, Partik S Wadhokar1, Ajitkumar Jadhav1

  • 1Department of Cardiology, Dr D Y Patil Medical College Hospital & Research Centre, Pimpri, Pune, India.

PubMed

Insights

Double chambered left ventricle (DCLV), a rare congenital heart defect, is often incidentally found. This case highlights how cardiac imaging can misdiagnose DCLV, revealing an anomalous muscle bundle instead.

Area of Science:

  • Cardiology
  • Congenital Heart Disease

Background:

  • Double chambered left ventricle (DCLV) is a rare congenital anomaly often diagnosed incidentally with a generally benign prognosis.
  • Accurate differentiation of DCLV from other cardiac abnormalities is critical due to potential clinical implications.
  • Limited data exists on the natural history, prognosis, complications, and treatment of DCLV.

Approach:

  • This case report details the evaluation of a young male presenting with palpitations.
  • Initial diagnosis of DCLV was made using 2D echocardiography.
  • Cardiac magnetic resonance imaging (CMR) was performed for further characterization.

Key Points:

  • CMR findings did not confirm DCLV but identified an anomalous apical basal muscle bundle (ABMB).
  • Atypical left ventricular (LV) trabecularization was observed, mimicking DCLV.
  • This case underscores the importance of advanced imaging in differentiating DCLV from similar cardiac morphologies.

Conclusions:

  • Advanced cardiac imaging like CMR is essential for accurate diagnosis and differentiation of DCLV.
  • Misdiagnosis of DCLV can occur, necessitating careful interpretation of imaging findings.
  • Further research is needed to clarify the clinical significance of conditions mimicking DCLV.