CT and histological findings of diffuse lipomatosis with a hemangioendothelioma: a case report

A 3 1/2-year-old boy with multiple soft tissue tumors and weakness of the right lower extremity is presented. Swelling of the right lower extremity was noted at 3 weeks, and soft masses at the hip at one year and in the inguinal region at 2 1/2 years of age. Right lower extremity weakness was noted about one year and non-progressive. CT scanning demonstrated characteristic subcutaneous lipomatosis with muscle involvement and a pelvic mass with positive enhancement that infiltrated into the spinal canal. Histological examination revealed diffuse lipomatosis involving muscles in the right hip mass and a lipoma with a hemangioendothelioma in the right inguinal mass. Diffuse lipomatosis combined with a lipoma and a hemangioendothelioma suggests a hamartomatous origin.