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Complicated Congenital Pulmonary Adenomatoid Malformation Type I following Right Lower Lobectomy: A Case Report
Preeti Basnet1, Anish Joshi1, Saurab Karki2
1Department of Pediatrics, Kathmandu University School of Medical Sciences, Dhulikhel, Kavrepalanchok, Nepal.
Insights
Congenital pulmonary airway malformation (CPAM) can cause serious illness in children. A 4-year-old girl with recurrent infections successfully underwent surgery for type I CPAM, highlighting the need for more research on symptomatic cases.
Area of Science:
- Pediatric Surgery
- Pulmonology
- Medical Imaging
Background:
- Congenital pulmonary airway malformation (CPAM) is a rare congenital lung defect impacting infants and children.
- CPAM can lead to significant respiratory issues and mortality, with variable presentation from birth to later in life.
- Surgical intervention is often necessary but carries risks, particularly in complex or symptomatic cases.
Observation:
- A 4-year-old female presented with recurrent chest infections.
- Imaging confirmed type I CPAM with a coexisting infection.
- The patient underwent a right lower lobe resection via posterolateral thoracotomy.
Findings:
- The surgical procedure for type I CPAM in this symptomatic pediatric patient was successful.
- The patient experienced a favorable outcome and recovered well post-operation.
- This case demonstrates successful management of a symptomatic CPAM case.
Implications:
- Further research is needed to establish consensus on surgical timing and outcomes for symptomatic CPAM patients.
- This case contributes to the understanding of surgical management in pediatric CPAM.
- Effective treatment of symptomatic CPAM can lead to positive patient outcomes.
Abstract:
Congenital pulmonary airway malformation is a rare congenital abnormality of the lungs. It can manifest at any age and can lead to significant morbidity and mortality in infants and children. Some individuals with congenital lung malformations may present with respiratory symptoms right after birth, while others may remain asymptomatic for extended periods. We present a case of a 4-year-old female child who experienced recurrent chest infections. Imaging revealed type I congenital pulmonary airway malformation with an underlying infection. Despite the increased risks associated with surgery and the complexity of the disease, the patient underwent a posterolateral thoracotomy with resection of the right lower lobe. The patient achieved successful outcomes and was able to recover successfully following the surgery. This case study holds significance because several studies have focused on the timing and outcomes of surgical intervention in asymptomatic cases, there remains a lack of consensus regarding symptomatic patients and their outcomes after surgery.
Keywords:
case reports; neonates; pneumonia.
