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Conduction System Pacing in Pediatrics and Congenital Heart Disease: A Case Report and Literature Review
Michael Scott1, Joseph S Needleman2, Adam C Kean1
1Division of Pediatric Cardiology, Department of Pediatrics, Indiana University School of Medicine, Indianapolis, IN, USA.
Insights
Left bundle branch pacing (LBBP) offers a safe alternative to right ventricular pacing for preventing cardiomyopathy. This study highlights LBBP
Area of Science:
- Cardiology
- Electrophysiology
- Pediatric Heart Disease
Background:
- Conduction system pacing, including His bundle pacing (HBP) and left bundle branch pacing (LBBP), is an alternative to right ventricular (RV) pacing.
- This pacing modality aims to prevent pacemaker-associated cardiomyopathy.
- LBBP has demonstrated safety and efficacy in pediatric populations in prior small studies.
Purpose of the Study:
- To present a case of successful left bundle branch pacing (LBBP) in a pediatric patient with congenital heart disease.
- To evaluate the transition from RV pacing to LBBP for improving left ventricular function.
- To provide a foundation for reviewing LBBP in pediatrics and congenital heart disease.
Main Methods:
- Case report detailing a patient with congenital atrioventricular block and cardiomyopathy post-ventricular septal defect repair.
- Transition of pacing from a right ventricular (RV) epicardial system to a left bundle branch pacing (LBBP) system.
- Assessment of left ventricular function post-pacing system change.
Main Results:
- The patient experienced improvement in left ventricular function after transitioning to LBBP.
- This suggests LBBP can be effective in pediatric patients with specific cardiac conditions.
- The case supports LBBP as a viable alternative to RV pacing in complex pediatric cases.
Conclusions:
- Left bundle branch pacing (LBBP) is a safe and effective alternative to right ventricular (RV) pacing in pediatric patients.
- LBBP can lead to significant improvement in left ventricular function in patients with congenital heart disease and cardiomyopathy.
- Further research and case reviews are warranted to establish LBBP's role in pediatric and congenital heart disease management.
Abstract:
Conduction system pacing involving either His bundle pacing (HBP) or left bundle branch pacing (LBBP) is a modality that has been introduced as a safe and effective alternative to right ventricular (RV) pacing to help prevent pacemaker-associated cardiomyopathy. While HBP has been employed in the pediatric and congenital populations, several small studies have shown LBBP to be safe and effective in the pediatric population. We present a patient with congenital atrioventricular block and postoperative ventricular septal defect repair cardiomyopathy with subsequent left ventricular function improvement following a transition from an RV epicardial pacemaker system to an LBBP system. This case report serves as a foundation for a review of the current state of LBBP in pediatrics and congenital heart disease.
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