Arrhythmogenic Left Ventricular Mass as the Initial Presentation of Cardiac Sarcoidosis

Erika Hutt1, Evan Whitehead1, Carmela D Tan1

  • 1Cardiovascular Medicine, Cleveland Clinic Foundation, Cleveland, Ohio, USA.

JACC. Case Reports
|March 29, 2024
PubMed

Insights

Left ventricular masses are rare, but cardiac sarcoidosis can mimic tumors. Cardiac magnetic resonance imaging is crucial for accurate diagnosis of these challenging cardiac conditions.

Area of Science:

  • Cardiology
  • Oncology
  • Radiology

Background:

  • Cardiac tumors in the left ventricle are uncommon clinical presentations.
  • Accurate diagnosis of cardiac masses is essential for appropriate patient management.
  • Cardiac magnetic resonance (CMR) offers superior soft-tissue characterization for cardiac imaging.

Observation:

  • A patient presented with arrhythmia and a left ventricular mass.
  • Initial evaluation suggested a cardiac tumor of the left ventricle.

Findings:

  • The left ventricular mass was ultimately diagnosed as cardiac sarcoidosis.
  • Cardiac sarcoidosis can present as a myocardial mass, mimicking primary or secondary cardiac tumors.
  • Tissue diagnosis is critical for differentiating infiltrative diseases from neoplasms.

Implications:

  • This case highlights the importance of considering infiltrative myocardial diseases, such as sarcoidosis, in the differential diagnosis of left ventricular masses.
  • Cardiac magnetic resonance imaging plays a pivotal role in evaluating cardiac masses and guiding diagnostic pathways.
  • A comprehensive diagnostic approach is necessary to avoid misdiagnosis and ensure optimal treatment for patients with cardiac masses.