Dural sinus malformation presenting with proptosis: report and review of a rare entity

Tejus M N Rao1, Sumit Thakar2, Paritosh Pandey3

  • 1Department of Neurosurgery, Sri Sathya Sai Institute of Higher Medical Sciences, Whitefield, ITPL Main Road, Bangalore, 560066, Karnataka, India.

Insights

Dural sinus malformation (DSM) can cause secondary proptosis. Endovascular embolization successfully treated a pediatric case, resolving eye proptosis and venous malformation.

Area of Science:

  • Vascular Malformations
  • Neuro-ophthalmology
  • Pediatric Neurology

Background:

  • Dural sinus malformation (DSM) is a rare condition involving dural venous sinus dilatation.
  • Secondary proptosis due to venous reflux from DSM is exceptionally rare, with few documented cases.

Observation:

  • A 17-month-old boy presented with progressive right eye proptosis.
  • The proptosis was attributed to a dural sinus malformation affecting the transverse sinus and torcula.

Findings:

  • Endovascular embolization was performed to address the arterio-venous fistula associated with the DSM.
  • Successful embolization led to complete thrombosis of the venous lake.
  • Significant improvement in the patient's proptosis was observed at the 6-month follow-up.

Implications:

  • This case highlights endovascular embolization as an effective treatment for DSM-induced proptosis.
  • The angio-architectural features of DSM are crucial for determining prognosis.
  • Further research into rare vascular malformations and their management is warranted.

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