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Plummer-Vinson syndrome: a rare occurrence in paediatrics
Wasif Ilyas Vohra1, Kamran Sadiq2, Mubashir Iqbal2
1Department of Paediatrics and Child Health, Aga Khan University Hospital, Karachi, Pakistan. dr.wasif17@gmail.com.
BMC Pediatrics
|April 27, 2024
Summary
Plummer-Vinson syndrome (PVS), a rare condition in children, involves anemia and dysphagia. Esophageal dilation is crucial for treating this rare pediatric case, improving growth and development.
Area of Science:
- Pediatric Gastroenterology
- Rare Diseases
Background:
- Plummer-Vinson syndrome (PVS) is a rare disorder characterized by anemia, esophageal webs, and dysphagia.
- Typically affects middle-aged women, with infrequent reports in pediatric populations.
Observation:
- A 1-year-old South Asian male presented with a 4-month history of dysphagia, anemia, and vomiting after eating.
- Blood tests confirmed microcytic hypochromic anemia.
- An esophagogram revealed upper thoracic esophageal narrowing, suggesting an esophageal web.
Findings:
- The patient was diagnosed with Plummer-Vinson syndrome.
- Esophageal dilation using a Savary-Gilliard dilator (5mm, 7mm, and 9mm probes) was performed.
- Iron supplements improved hemoglobin levels but did not resolve dysphagia.
Implications:
- Early recognition and high suspicion of PVS are vital in pediatric cases.
- Esophageal dilation is essential for relieving dysphagia and enabling proper nutrition.
- Timely intervention supports improved growth and development in affected children.
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