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Updated: Jun 20, 2026
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Morphological and Functional Assessment of the Right Ventricle Using 3D Echocardiography
Published on: October 28, 2020
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Arrhythmogenic right ventricular cardiomyopathy: Unveiling clinical presentations, CMR insights and prognosis in a
Anum Yousaf1, Muhammad Fawad Tahir2, Ummarah Kamran1
1Department of Radiology, Rawalpindi Institute of Cardiology, Rawalpindi, Pakistan.
Current Problems in Cardiology
|May 9, 2024
Summary
Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) presents differently in Pakistan. Early detection and improved diagnostic facilities, including cardiac magnetic resonance (CMR), are crucial for this hereditary heart condition.
Area of Science:
- Cardiology
- Genetics
- Medical Diagnostics
Background:
- Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is a hereditary condition affecting 1 in 2000-5000 individuals.
- It is a major cause of sudden cardiac death in young people and athletes.
- Definitive diagnosis of ARVC remains challenging.
Purpose of the Study:
- To evaluate the clinical presentations, electrocardiogram (ECG) findings, and imaging characteristics of ARVC patients in Pakistan.
- To compare findings with existing international literature.
- To highlight the role of cardiac magnetic resonance (CMR) in ARVC diagnosis.
Main Methods:
- A single-center retrospective study of ARVC patients from 2021-2023.
- Inclusion of the Task Force Criteria for diagnosis.
- Analysis of patient presentations, ECG, and CMR data.
Main Results:
- The study reports divergent symptom prevalence compared to current literature.
- Cardiac magnetic resonance (CMR) plays a critical role in diagnosis.
- A significant mortality rate of 17% was observed in the cohort.
Conclusions:
- Early detection and improved diagnostic facilities are essential for managing ARVC in the region.
- CMR is vital for accurate ARVC diagnosis, despite limited global access.
- Further research on ARVC in Pakistan is warranted.
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