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[Treatment of haemophilia in Austria]

Christoph Male1, Cihan Ay2, Richard Crevenna3

  • 1Universitätsklinik für Kinder- und Jugendheilkunde, Medizinische Universität Wien, Währinger Gürtel 18-20, 1090, Wien, Österreich. christoph.male@meduniwien.ac.at.

Wiener Klinische Wochenschrift
|May 14, 2024
PubMed

This guideline is intended to provide practical guidance for the diagnosis and treatment of haemophilia in Austria. Few randomized controlled interventional trials are available addressing the treatment of haemophilia, therefore recommendations are usually based on low level of evidence and represent expert consensus.This guideline is based on the WFH guideline, published in 2020, and adapted according to the national circumstances and experience.It includes recommendations and suggestions for diagnosis and follow-up visits and pharmacological therapies for treatment and prophylaxis. Further topics comprise special aspects in children and adults with severe haemophilia, outcome measurement, and management of trauma, special bleedings and interventions, including dental procedures, inhibitors, management of haemophilia carriers, and psychosocial aspects.

Keywords:
AntifibrinolyticsClotting Factor ConcentratesDesmopressinGuidelineHaemophiliaInhibitorsNon-Replacement TherapiesOutcomes

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