Low-grade malignant peripheral nerve sheath tumour presenting as retroperitoneal spindle cell neoplasm
Mitesh Karn1, Basant Kumar Mahato1, Liladhar Ojha1
1Department of Medicine, Gandaki Medical College Teaching Hospital and Research Centre, Pokhara, Gandaki Province, Nepal.
Abstract:
Retroperitoneal spindle cell neoplasms are diagnostically challenging. Malignant peripheral nerve sheath tumours (MPNSTs) can sometimes present as sporadic primary retroperitoneal tumours. MPNSTs are usually high-grade and highly aggressive tumours and are associated with a poor prognosis. Low-grade MPNSTs are very rarely described. This current case report describes a case of sporadic primary low-grade MPNST presenting as retroperitoneal spindle cell neoplasm. The diagnosis, imaging and immunohistopathological findings, as well as its successful surgical management, are presented.
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