Multiple recurrent supraventricular tachycardia in infantile tuberous sclerosis complex: management requiring
Xander Jacquemyn1,2, Shelby Kutty1, Mitchell I Cohen3
1Department of Pediatrics, Helen B. Taussig Heart Center, Johns Hopkins Hospital, Baltimore, MD, USA.
Abstract:
We report the case of a female neonate admitted to the neonatal ICU with a rapid, narrow-complex tachyarrhythmia determined to be supraventricular tachycardia. Multimodality imaging and genetic testing confirmed a diagnosis of tuberous sclerosis complex with multiple cardiac rhabdomyomas. At 13 days of age, the patient was readmitted, exhibiting recurrent supraventricular tachycardia non-responsive to first-line treatment. Management required triple-drug therapy, whereafter the patient remained stable without recurrences. This is a rare report of supraventricular tachycardia in a functionally normal heart with the occurrence of supraventricular tachycardia due to structural abnormalities, with the possibility of multiple concealed accessory pathways.
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