Biventricular function after Ebstein anomaly repair from a single-center echocardiography study.

Area of Science:

• Cardiology
• Cardiac Surgery
• Echocardiography

Background:

• Ebstein anomaly (EbA) is a congenital heart defect affecting the tricuspid valve.
• Surgical correction aims to improve biventricular function and valve durability.
• Understanding biventricular remodeling post-EbA surgery is crucial for patient management.

Purpose of the Study:

• To evaluate biventricular remodeling and function after Ebstein anomaly surgical correction.
• To correlate echocardiographic findings with Ebstein anomaly types (Carpentier classification).
• To assess the mid-term outcomes of EbA surgical repair.

Main Methods:

• Retrospective study of 110 Ebstein anomaly patients (April 2015 - August 2022).
• Classification based on Carpentier criteria into types A/B (Group 1) and C/D (Group 2).
• Echocardiography performed preoperatively, early, and mid-term postoperatively for 78 surgically corrected patients.

Main Results:

• Mid-term follow-up showed minimal moderate/severe tricuspid regurgitation (9.1%).
• Group 2 (EbA types C/D) experienced initial RV systolic dysfunction post-surgery, with slow recovery over 12 months.
• Group 1 (EbA types A/B) maintained stable biventricular systolic function postoperatively.

Conclusions:

• Surgical Ebstein anomaly correction achieves high success rates and durable valve function.
• Biventricular systolic function is well-preserved in EbA types A/B post-surgery.
• EbA types C/D exhibit transient RV dysfunction followed by recovery, with preserved LV function.