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Mid-aortic syndrome presented as dilated cardiomyopathy
Kah Yit Pang1, Putri Yubbu2,3, Norliza Ali3
1Department of Paediatric, Faculty of Medicine and Health Sciences, University Putra Malaysia, Serdang, Malaysia.
BMJ Case Reports
|June 20, 2024
Summary
Mid-aortic syndrome (MAS), a rare vascular condition, can cause heart failure. Early diagnosis via echocardiography and CT angiography is crucial for effective treatment and improved cardiac function.
Area of Science:
- Cardiovascular Medicine
- Pediatric Cardiology
- Vascular Surgery
Background:
- Mid-aortic syndrome (MAS) is a rare vascular disease typically causing renovascular hypertension and lower extremity arterial insufficiency.
- Dilated cardiomyopathy is an uncommon manifestation of MAS.
Observation:
- A pediatric patient presented with congestive heart failure initially diagnosed as dilated cardiomyopathy.
- Subsequent echocardiography revealed abnormal Doppler findings, raising suspicion for MAS.
- CT angiography confirmed thoracic coarctation, a key feature of MAS.
Findings:
- The patient had a discrete thoracic coarctation measuring 2.1 mm in diameter.
- Inflammatory and connective tissue markers were negative.
- Successful aortic coarctation stenting led to improved cardiac function.
Implications:
- Highlights the importance of considering MAS in pediatric cases of dilated cardiomyopathy.
- Emphasizes the role of vigilant clinical and echocardiogram assessment in diagnosing MAS.
- Demonstrates that MAS is a treatable cause of heart failure in children.
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